Orofacial assessment of children with Prader-Willi Syndrome
DOI:
https://doi.org/10.47990/alop.v11i2.258Keywords:
Prader-Willi syndrome, Skull/growth and development, Facial bones/growth and development, Oral health, Special needsAbstract
Aim: To assess the oral health status and craniofacial growth of patients with Prader-Willi Syndrome (PWS), compared to obese non-PWS children controls.
Methods and Result: Were selected 40 PWS children and 40 non-PWS obese controls, aged 10.9 years (control: 11.89 years) and BMI 22.72kg/m2 (control 36.43 kg/m2). Were assessed the number of teeth, type of dentition, presence of caries, gingival bleeding, malocclusion, plaque accumulation, dental erosion, gingival hyperplasia, and enamel hypoplasia. Questionnaires assessed oral hygiene habits. Panoramic radiographs assessed craniofacial growth.
The case group had a 6.8% lower number of teeth compared to the control group. A statistically significant difference was seen in gingival bleeding, dental erosion and enamel hypoplasia (p=0,009; p=0,02 and p=0,006; respectively). There were no statistically significant differences, it was observed an augmented number of carious lesions and dental crowding in PWS children (p=0,35 and p=0,07). Both groups showed poor dental hygiene. PWS children showed augmented mandibular ramus growth with a statistically significant difference (p=0.03).
Conclusion: PWS children had statically augmented gingival bleeding and enamel hypoplasia than non-PWS obese controls. PWS children may present increased craniofacial vertical growth. Further investigations are needed for this population.
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