Prosthetic rehabilitation in pediatric patient with ectodermal dysplasia

Abstract

Introduction. Ectodermal dysplasia is a congenital disorder characterized by the abnormal development of two or more ectoderm derivatives, such as hair, sweat glands, nails and teeth. The most common types are Hypohydrotic / Anhydrotic and Hydrotic. The objective of the case report is to show the characteristics of a patient with Ectodermal Anhydrotic Dysplasia, as well as the dental treatment performed and the results achieved. Case Report. A 5-year-old male patient with ectodermal anhydrotic dysplasia goes with his mother to the Pediatric dentistry clinic at ENES UNAM León, who reports as a reason for consultation “of having teeth placed”. In the extraoral exam, there is an evident lack of eyebrows and eyelashes, thin hair, prochelia and decreased lower facial third is observed. Within the intraoral evaluation, oligodontia is observed along with a conical shape of teeth 52 and 62. In the panoramic radiography, the presence of teeth 11 and 21 is observed. Dental diagnosis. Oligodontia, conical teeth, delayed eruption, narrow atrophic alveolar rim, and decreased vertical dimension. Treatment. Rehabilitation with a removable partial prosthesis with expansion screw in the upper jaw along with lithium disilicate crowns on teeth 52 and 62, and a complete denture prosthesis with an expansion screw in the lower jaw. Results. A better masticatory function, phonation, lingual peristalsis and greater patient self-esteem were achived. Conclusion. Early rehabilitation and   integral treatment promotes the growth of the oral structures, function, aesthetics and self-esteem of the patient.